Abstract

An atypical teratoid rhabdoid tumor (ATRT) is a pediatric embryonic tumor of the central nervous system and is uncommon in adults. We report a case of a 33-year-old female who presented with multiple dural lesions that were diagnosed as ATRT. She had a past history of endoscopic transnasal transsphenoidal and subsequent transcranial decompression of suprasellar lesion 6 months prior, with a presumptive diagnosis of atypical pituitary adenoma, which on retrospective evaluation was confirmed as sellar ATRT. Adult sellar ATRT, though rare, has now been proposed as a distinct clinicopathological and genetic variant that is predominantly seen in middle-aged women. We discuss the uniqueness of this rare aggressive tumor with reference to the age, location, and the challenges faced in the clinical and pathological diagnosis.

Author Details

Authors

• Radhika Mhatre¹
• Akshay Kulkarni²
• Priyanka Sajiv¹
• Andiperumal Raj Prabhuraj²
• Bevinahalli N. Nandeesh¹

Departments

• ¹ Department of Neuropathology, and
• ² Department of Neurosurgery, National Institute of Mental Health and Neurosciences (NIMHANS), Bangalore, India

Address

Dr. Bevinahalli N. Nandeesh, Associate Professor
Department of Neuropathology
National Institute of Mental Health and Neurosciences (NIMHANS)
Bangalore 560029, India
Email: nandeeshbn@
gmail.com

Citation